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The “world” of soft tissue sarcomas is a highly complex one, due to the large range of tumor types, each of which is characterized by specific features in terms of its epidemiology, pathology diagnosis, clinical behavior, therapy and biomarker pattern (of both diagnostic and therapeutic value). This book offers a practical, clearly structured reference guide, covering all of these aspects for each soft tissue tumor. Thanks to the consistent and user-friendly format, readers can quickly and easily find the information they need; in addition, up-to-date and authoritative literature information helps them to pursue further research.
Overall, this book offers professionals and residents in the fields of oncology, surgery, and pathology an essential guide for study, review, and everyday clinical practice.
Definition
Pages 3-4
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Epidemiology and Presentation
Pages 5-9
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Etiology and Predisposition
Pages 11-15
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Pathology
Pages 17-24
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Biomarkers
Pages 25-26
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Prognosis
Pages 27-32
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Therapy
Pages 33-47
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Acoustic Neuroma
Pages 51-54
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Acquired Digital Fibrokeratoma
Pages 55-56
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Acral Fibromyxoma
Pages 57-58
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Adult Fibrosarcoma
Pages 59-61
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Adult Rhabdomyoma
Pages 63-64
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Alveolar Rhabdomyosarcoma
Pages 65-67
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Alveolar Soft Part Sarcoma
Pages 69-72
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Anastomosing Hemangioma
Pages 73-74
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Aneurysmal Fibrous Histiocytoma
Pages 75-76
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Angiofibroma
Pages 77-77
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Angiofibroma of Soft Tissue
Pages 79-81
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Angiokeratoma
Pages 83-84
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Angioleiomyoma
Pages 85-86
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Angiolipoma
Pages 87-88
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Angiomatoid Fibrous Histiocytoma
Pages 89-91
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Angiomyofibroblastoma
Pages 93-94
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Angiomyolipoma
Pages 95-97
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Angiosarcoma
Pages 99-103
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Angiomatosis
Pages 105-107
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Angiomyxoma
Pages 109-109
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Arteriovenous Malformation Hemangioma
Pages 111-113
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Atypical Fibrous Histiocytoma
Pages 115-116
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Atypical Fibroxanthoma
Pages 117-119
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Atypical Lipomatous Tumor
Pages 121-121
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Atypical Vascular Lesion
Pages 123-124
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BCOR-Rearranged Sarcoma
Pages 125-125
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Benign Fibrous Histiocytoma
Pages 127-130
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Benign Metastasizing Leiomyoma
Pages 131-132
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Benign Triton Tumor
Pages 133-134
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Biphenotypic Sinonasal Sarcoma
Pages 135-137
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Bladder Soft Tissue Tumors
Pages 139-139
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Breast Angiosarcoma
Pages 141-143
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Breast Phyllodes Tumor
Pages 145-147
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Breast Soft Tissue Tumors
Pages 149-149
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Calcifying Aponeurotic Fibroma
Pages 151-152
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Calcifying Fibrous Tumor
Pages 153-154
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Cardiac Soft Tissue Tumors
Pages 155-156
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Cardiac Myxoma
Pages 157-158
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Cardiac Rhabdomyoma
Pages 159-161
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Cellular Angiofibroma
Pages 163-164
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Cellular Fibrous Histiocytoma
Pages 165-166
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Cherry Hemangioma
Pages 167-168
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Chondroid Lipoma
Pages 169-170
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CIC-Rearranged Sarcoma
Pages 171-171
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Clear Cell Sarcoma
Pages 173-176
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Clear Cell Sugar Tumor
Pages 177-178
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Composite Hemangioendothelioma
Pages 179-180
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Congenital Hemangioma
Pages 181-183
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Congenital Mesoblastic Nephroma
Pages 185-188
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Cutaneous Angiofibroma
Pages 189-192
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Cutaneous Angiosarcoma
Pages 193-193
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Cutaneous Epithelioid Angiomatous Nodule
Pages 195-197
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Cutaneous Fibroepithelial Polyp
Pages 199-200
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Cutaneous Leiomyoma
Pages 201-203
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Cutaneous Leiomyosarcoma
Pages 205-207
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Dedifferentiated Liposarcoma
Pages 209-212
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Deep Angiomyxoma
Pages 213-215
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Dermal Nerve Sheath Myxoma
Pages 217-219
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Dermatofibroma
Pages 221-221
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Dermatofibrosarcoma Protuberans
Pages 223-227
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Dermatomyofibroma
Pages 229-230
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Desmoid-Type Fibromatosis
Pages 231-237
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Desmoplastic Fibroblastoma
Pages 239-240
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Desmoplastic Small Round Cell Tumor
Pages 241-243
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Diffuse Pulmonary Lymphangiomatosis
Pages 245-246
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Diffuse Tenosynovial Giant Cell Tumor
Pages 247-250
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Digestive System Soft Tissue Tumors
Pages 251-252
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EBV-Associated Smooth Muscle Tumor
Pages 253-254
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Disseminated Peritoneal Leiomyomatosis
Pages 255-256
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Ectomesenchymoma
Pages 257-258
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Ectopic Hamartomatous Thymoma
Pages 259-260
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Ectopic Meningioma
Pages 261-264
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Elastofibroma
Pages 265-266
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Embryonal Rhabdomyosarcoma
Pages 267-270
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Endometrial Stromal Sarcoma
Pages 271-274
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Epithelioid Fibrous Histiocytoma
Pages 275-277
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Epithelioid Hemangioendothelioma
Pages 279-281
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Epithelioid Hemangioma
Pages 283-284
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Epithelioid Sarcoma
Pages 285-288
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Esophageal Leiomyoma
Pages 289-291
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Ewing-Like Sarcomas
Pages 293-297
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Extrarenal Rhabdoid Tumor
Pages 299-301
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Extraskeletal Aneurysmal Bone Cyst
Pages 303-304
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Extraskeletal Chondroma
Pages 305-306
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Extraskeletal Chordoma
Pages 307-310
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Extraskeletal Ewing Sarcoma
Pages 311-316
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Extraskeletal Myxoid Chondrosarcoma
Pages 317-319
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Extraskeletal Osteosarcoma
Pages 321-323
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Fetal Rhabdomyoma
Pages 325-327
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Fibroma
Pages 329-329
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Fibroma of Tendon Sheath
Pages 331-332
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Fibromatosis
Pages 333-333
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Fibromatosis Colli
Pages 335-336
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Fibro-Osseous Pseudotumor of Digits
Pages 337-337
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Fibrosarcoma
Pages 339-339
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Fibrous Hamartoma of Infancy
Pages 341-342
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Fibrous Histiocytoma
Pages 343-343
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Gardner Fibroma
Pages 345-347
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Gastrointestinal Clear Cell Sarcoma
Pages 349-351
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Gastrointestinal Soft Tissue Tumors
Pages 353-353
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Gastrointestinal Stromal Tumor (GIST)
Pages 355-367
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Genital Rhabdomyoma
Pages 369-370
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Giant Cell Fibroblastoma
Pages 371-372
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Giant Cell Tumor
Pages 373-375
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Glomeruloid Hemangioma
Pages 377-378
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Glomus Tumor
Pages 379-382
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Granular Cell Tumor
Pages 383-386
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Hemangioblastoma
Pages 387-388
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Hemangioendothelioma
Pages 389-389
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Hemangioma
Pages 391-393
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Hemosiderotic Fibrolipomatous Tumor
Pages 395-396
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Hepatic Angiosarcoma
Pages 397-398
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Hepatic Calcifying Nested Stromal Epithelial Tumor
Pages 399-401
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Hepatic Embryonal Sarcoma
Pages 403-405
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Hepatic Epithelioid Hemangioendothelioma
Pages 407-409
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Hepatic Hemangioma
Pages 411-413
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Hepatic Mesenchymal Hamartoma
Pages 415-417
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Hibernoma
Pages 419-420
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High-Grade Endometrial Stromal Sarcoma
Pages 421-421
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Hobnail Hemangioma
Pages 423-424
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Hybrid Nerve Sheath Tumor
Pages 425-426
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Inclusion Body Fibromatosis
Pages 427-428
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Infantile Fibrosarcoma
Pages 429-431
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Infantile Hemangioma
Pages 433-436
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Inflammatory Fibroid Polyp
Pages 437-438
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Inflammatory Myofibroblastic Tumor
Pages 439-442
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Intimal Sarcoma
Pages 443-444
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Intramuscular Hemangioma
Pages 445-446
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Intramuscular Myxoma
Pages 447-448
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Ischemic Fasciitis
Pages 449-450
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Juvenile Hyaline Fibromatosis
Pages 451-452
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Juxta-Articular Myxoma
Pages 453-454
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Juxtaglomerular Cell Tumor
Pages 455-456
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Kaposiform Hemangioendothelioma
Pages 457-458
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Kaposi Sarcoma
Pages 459-463
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Kidney Clear Cell Sarcoma
Pages 465-467
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Kidney Rhabdoid Tumor
Pages 469-469
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Kidney Soft Tissue Tumors
Pages 471-471
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Leiomyoma
Pages 473-473
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Leiomyoma of Deep Tissue
Pages 475-476
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Leiomyosarcoma
Pages 477-481
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Lipoblastoma
Pages 483-484
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Lipofibromatosis
Pages 485-486
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Lipofibromatosis-Like Neural Tumor
Pages 487-489
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Lipoma
Pages 491-494
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Lipomatosis
Pages 495-498
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Lipomatosis of Nerve
Pages 499-500
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Liposarcoma
Pages 501-503
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Littoral Cell Angioma
Pages 505-506
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Localized Tenosynovial Giant Cell Tumor
Pages 507-508
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Low-Grade Endometrial Stromal Sarcoma
Pages 509-509
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Low-Grade Fibromyxoid Sarcoma
Pages 511-513
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Low-Grade Myofibroblastic Sarcoma
Pages 515-517
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Lung Chondroma
Pages 519-520
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Lung Soft Tissue Tumors
Pages 521-521
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