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Orphan Lung Diseases from Definition to Organisation of Care
Pages 1-3
Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease provides a comprehensive, clinically focused textbook on rare and so-called ‘orphan’ pulmonary diseases. The book is oriented towards the diagnostic approach, including manifestations suggesting the disease, diagnostic criteria, methods of diagnostic confirmation, and differential diagnosis, with an overview of management.
Orphan Lung Diseases from Definition to Organisation of Care
Pages 1-3
The Challenges of Clinical Research in Orphan Diseases
Pages 5-15
Chronic Bronchiolitis in Adults
Pages 17-27
“Diffuse Bronchiectasis of Genetic Origin”
Pages 29-51
Allergic Bronchopulmonary Mycosis
Pages 53-71
Orphan Tracheopathies
Pages 73-89
Amyloidosis and the Respiratory Tract
Pages 91-111
Eosinophilic Granulomatosis with Polyangiitis (Churg-Strauss Syndrome): A Clinical and Therapeutic Approach
Pages 113-125
Granulomatosis with Polyangiitis (Wegener’s Granulomatosis)
Pages 127-153
Alveolar Hemorrhage
Pages 155-175
Pulmonary Involvement in Takayasu Arteritis and Behçet Disease
Pages 177-190
Pulmonary Vascular Manifestations of Hereditary Hemorrhagic Telangiectasia
Pages 191-200
Hepatopulmonary Syndrome
Pages 201-210
Non-langerhans Cell Histiocytosis-Including Erdheim-Chester Disease- and the Lung
Pages 211-226
Eosinophilic Pneumonia
Pages 227-251
Multiple Cystic Lung Diseases
Pages 253-270
Lymphangioleiomyomatosis
Pages 271-283
Pulmonary Alveolar Proteinosis
Pages 285-294
Exogenous Lipoid Pneumonia
Pages 295-303
Pulmonary Alveolar Microlithiasis
Pages 305-313
Pulmonary Fibrosis and the Many Faces of UIP
Pages 315-325
The Syndrome of Combined Pulmonary Fibrosis and Emphysema
Pages 327-347
Non-specific, Unclassifiable, and Rare Idiopathic Interstitial Pneumonia: Acute Interstitial Pneumonia, Respiratory Bronchiolitis Interstitial Pneumonia, Desquamative Interstitial Pneumonia, Nonspecific Interstitial Pneumonia
Pages 349-362
Organizing Pneumonias
Pages 363-378
Interstitial Lung Disease in Systemic Sclerosis
Pages 379-390
Interstitial Lung Disease in Connective Tissue Diseases Other Than Systemic Sclerosis
Pages 391-418
Interstitial Lung Disease in Undifferentiated Forms of Connective Tissue Disease
Pages 419-434
Pulmonary Langerhans Cell Histiocytosis and Smoking-Related Interstitial Lung Diseases
Pages 435-456
Rare Causes and the Spectrum of Hypersensitivity Pneumonitis
Pages 457-472
Chronic Beryllium Disease and Other Interstitial Lung Diseases of Occupational Origin
Pages 473-491
Lymphoproliferative Lung Disorders
Pages 493-515
Pulmonary Manifestations of Hematological Malignancies: Focus on Pulmonary Chronic Graft-Versus Host Disease
Pages 517-527
Pulmonary Hypertension in Orphan Lung Diseases
Pages 529-539
Rare and Emergent Drug-Induced and Iatrogenic Respiratory Conditions: A Guide to Their Recognition and Management
Pages 541-580
From Cancer Mimicking Orphan Lung Disease to Orphan Thoracic Oncology
Pages 581-596
Rare Diffuse Lung Diseases of Genetic Origin
Pages 597-609
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