Titolo: Humoral Primary Immunodeficiencies

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Immunologia e Allergologia

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Humoral Primary Immunodeficiencies

Editore

Springer

Anno

2019

Pagine

387

ISBN

9783319917849

I prezzi indicati possono subire variazioni poiché soggetti all'oscillazione dei cambi delle valute e/o agli aggiornamenti effettuati dagli Editori.

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This book presents detailed state of the art knowledge on the humoral primary immunodeficiencies (PIDs), i.e., disorders arising from impaired antibody production due to defects intrinsic to B cells or defective interaction between B and T cells. There is extensive coverage of both basic science discoveries and the latest clinical advances in the field. The book is structured in accordance with the most recent classification of PIDs and also covers updates on the B cell immunological synapse. Readers will find comprehensive, in-depth descriptions of novel humoral PID genes and related clinical applications, mucosal B cells, and the various clinical phenotypes of humoral PIDs. Aspects such as differential diagnosis, clinical management in children and adults, and the role of vaccines are also addressed. The authors are all recognized experts from Europe, Australia, and the United States. Humoral Primary Immunodeficiencies will be of high value for immunologists, pediatricians, rheumatologists, oncologists, internists, and infectious disease specialists and will also be informative for MD and PhD students.

The B-Side of the Immune Response

Patrussi, Laura (et al.)

Pages 1-20
Mucosal B Cells

Troilo, Arianna (et al.)

Pages 21-34
CVID

Salzer, Ulrich

Pages 35-55
Late-Onset Combined Immunodeficiencies (LOCID)

López-Granados, Eduardo

Pages 57-66
Genetics of CVID

Lougaris, Vasssilios (et al.)

Pages 67-76

ICOS Deficiency

Salzer, Ulrich

Pages 77-82
CD19 Deficiency due to Genetic Defects in the CD19 and CD81 Genes

Zelm, Menno C. (et al.)

Pages 83-95
Genetic CD21 Deficiency

Thiel, Jens

Pages 97-99
TACI Deficiency

Bergbreiter, Astrid (et al.)

Pages 101-112
LRBA Deficiency

Gámez-Díaz, Laura

Pages 113-129
BAFF Receptor Deficiency

Smulski, Cristian R. (et al.)

Pages 131-147
TWEAK Deficiency

Salzer, Ulrich

Pages 149-152
NFKB2 Defects

Jacob, Shancy P. (et al.)

Pages 153-165
The WHIM Syndrome

Roselli, Giuliana (et al.)

Pages 167-177
Class-Switch Recombination Defects

Burg, Mirjam (et al.)

Pages 179-199
Selective IgA Deficiency

Sofia Appelberg, K. (et al.)

Pages 201-215
IgG Subclass and Anti-polysaccharide Antibody Deficiency

Vries, Esther

Pages 217-225
Good’s Syndrome (GS): Thymoma with Immunodeficiency

Peter, Hans-Hartmut

Pages 227-234
Differential Diagnosis in Hypogammaglobulinemia

Quinti, Isabella (et al.)

Pages 235-252
Management of Humoral Primary Immunodeficiencies in Pediatrics

Azzari, Chiara (et al.)

Pages 253-274
Management of Humoral Primary Immunodeficiencies in Adults

Vitiello, Gianfranco (et al.)

Pages 275-289
Vaccines in Humoral Primary Immunodeficiencies

Lodi, Lorenzo (et al.)

Pages 291-313
Malignancy in Predominantly Antibody Deficiencies (PAD)

Wehr, Claudia

Pages 315-323
Humoral Primary Immunodeficiency and Autoimmune and Inflammatory Manifestations

Janda, Aleš (et al.)

Pages 325-346
Chest Complications in Patients with Primary Antibody Deficiency Syndromes (PADS)

Chapel, Helen M., MA. MD. FRCP. FRCPath (et al.)

Pages 347-359