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Congenital Bleeding Disorders 2nd edition
Diagnosis and Management
Dorgalaleh
Editore
Springer
Anno
2023
Pagine
463
ISBN
9783031431555
200,00 €

DA SCONTARE

I prezzi indicati possono subire variazioni poiché soggetti all'oscillazione dei cambi delle valute e/o agli aggiornamenti effettuati dagli Editori.

This significantly updated new edition describes in detail the clinical presentations, diagnosis, and management of a wide range of congenital bleeding disorders. It will assist readers in overcoming the significant challenges involved in clinical and laboratory diagnosis and in providing effective clinical care that makes optimal use of new products, including recombinant factor concentrate. The coverage ranges from hemophilia A and B and von Willebrand disease to rare bleeding disorders such as congenital factor V, factor X, factor XI, and factor XIII deficiency and inherited platelet function disorders. The exceptional attention to rarer conditions is of particular importance given the considerable risk of overlooking them during diagnosis, with potential consequences for disease-related morbidity and mortality. The authors are acknowledged specialists in the field from across the world who have particular expertise in the disorder that they discuss. The book will be of value to hematologists, oncologists, pediatricians, laboratory specialists and technicians, general physicians, and trainees.

  1. Front Matter

    Pages i-xvi

    PDF

  2. An Overview of Hemostasis and Congenital Bleeding Disorders

    1. Front Matter

      Pages 1-1

      PDF

    2. An Overview of Hemostasis

      • Maryam Daneshi, Jamal Rashidpanah, Fatemeh Narouei

      Pages 3-27

    3. Congenital Bleeding Disorders: Diagnosis and Management

      • Akbar Dorgalaleh, Maryam Daneshi, Ali Dabbagh, Kendall P. Crookston

      Pages 29-74

  3. Common Bleeding Disorders

    1. Front Matter

      Pages 75-75

      PDF

    2. von Willebrand Disease: An Update on Diagnosis and Treatment

      • Emmanuel J. Favaloro

      Pages 77-105

    3. Hemophilia A: Diagnosis and Management

      • Zühre Kaya, Nader Safarian, Behnaz Pezeshkpoor, Dorothy M. Adcock

      Pages 107-143

    4. Hemophilia B: Diagnosis and Management

      • Giancarlo Castaman, Hoda Motlagh, Behnaz Pezeshkpoor

      Pages 145-171

  4. Rare Bleeding Disorders

    1. Front Matter

      Pages 173-173

      PDF

    2. Congenital Fibrinogen Disorders, Diagnosis, and Management

      • Alessandro Casini

      Pages 175-190

    3. Congenital Prothrombin Deficiency: Diagnosis and Management

      • Raimondo De Cristofaro

      Pages 191-209

    4. Congenital Factor V Deficiency, Diagnosis, and Management

      • Shadi Tabibian, Rodney M. Camire

      Pages 211-229

    5. Combined Factor V and Factor VIII Deficiency, Diagnosis, and Management

      • Elena Yakovleva

      Pages 231-248

    6. Vitamin K-Dependent Coagulation Factors Deficiency, Diagnosis, and Management

      • Maryam Sadat Hosseini, Mariasanta Napolitano

      Pages 249-258

    7. Congenital Factor VII Deficiency, Diagnosis, and Management

      • Mahmood Shams

      Pages 259-285

    8. Congenital Factor X Deficiency, Diagnosis, and Management

      • Fateme Roshanzamir, Magy Abdelwahab

      Pages 287-341

    9. Congenital Factor XI Deficiency, Diagnosis and Management

      • Simon Davidson

      Pages 343-362

    10. Congenital Factor XIII Deficiency, Diagnosis, and Management

      • Akbar Dorgalaleh

      Pages 363-375

  5. Inherited Platelet Function Disorders

    1. Front Matter

      Pages 377-377

      PDF

    2. Glanzmann Thrombasthenia: Diagnosis and Management

      • Man-Chiu Poon, Seyed Mehrab Safdari

      Pages 379-422

  6. Inherited Platelet Function Disorders

    1. Bernard-Soulier Syndrome: Diagnosis and Management

      • Bahare Ghasemi, Akbar Dorgalaleh

      Pages 423-444

    2. Gray Platelet Syndrome: Diagnosis and Management

      • Fatemeh Kianinodeh, Maryam Sadat Hosseini, Barbara J. Bain

      Pages 445-463

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